Evidence-based Guideline: Diagnosis and Treatment of Limb ...

Oct 12, 2014 · Weakness progresses slowly, with an average of 10 years before involvement of finger extensors and neck flexors, and later development of proximal extremity weakness.e474,e475,e478,e483 Neck flexor weakness is a distinguishing feature from other distal myopathies and was reported in 20%–100% of cases in various series.e474,e478,e483 Mild ... ................
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