Dystrophin-Deficient Cardiomyopathy
monary support, have significantly improved the life TABLE 1 DMD Versus BMD DMD BMD Dystrophin protein Absent Partially functional Incidence 1:5,000 male births 1:19,000 Mean age at onset, yrs 3–512 Mean age of becoming nonambulatory, yrs w12 w27 Mean life expectancy, yrs Mid to late 20s 40s Onset of cardiomyopathy, yrs 16–18 Variable ... ................
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