Ingrid Bockelmann
Ingrid Bockelmann
Peter’s Anomaly
(anterior chamber cleavage syndrome, mesodermal dysgenesis of cornea)
Peter’s anomaly is a congenital anomaly in which the iris (colored part of the eye) adheres to the innermost layers of the cornea (transparent front part of the eye that covers the iris and pupil), causing the center of the cornea to be malformed, hazy and white.
Parts of the Visual System Affected
Cornea is malformed, hazy and white (both corneas usually affected).
Optic nerve and retinal nerve fibers become damaged.
Effects of Peter’s Anomaly on the Visual System
Reduced visual acuity – inability to distinguish object details and shape.
Increased sensitivity to bright light.
Glaucoma – increased pressure inside the eye due to adhesions on eye, resulting in optic nerve and retinal nerve fiber damage and visual defects.
Amblyopia (“lazy eye”) - decreased vision despite healthy retina and visual pathways due to the inability of affected eye to “learn” to see clearly early in life.
Nystagmus – roving, involuntary eye movement.
Microphthalmia – abnormally small eye.
Retinal detachment – retina separates from the back of the eyeball.
Common Treatments
Wearing glasses or contacts to help with blurred vision.
Wearing dark glasses or a hat to help with glare.
Genetic counseling to help prevent future children from becoming affected.
Eye drops for symptoms of glaucoma.
Surgery to reduce the pressure inside the eye resulting from glaucoma.
Surgery to graft donated corneas onto the eyes if both corneas are very hazy and vision is very blurred. Corneal graft surgery can keep a child from developing amblyopia if the child is old enough to relate his/her level of vision correctly.
Surgery not recommended if only one eye affected.
Anticipated Functional Implications of Peter’s Anomaly
Need for low vision aids (glasses, contacts, magnifiers) as well as sunglasses or a hat.
Need for increased print size for reading and school work.
Assistance in recognizing smaller objects.
Assistance in recognizing the facial expressions of others in order to respond appropriately.
References
Bishop, V.E. (1996). Preschool children with visual impairments. Retrieved July 5, 2008, from
Cassin, B., & Rubin, M.L. (Ed.). (2006). Dictionary of eye terminology (5th ed.). Gainesville, FL: Triad.
Goldberg, S., & Trattler, T. (2008). Ophthalmology made ridiculously simple (4th ed.). Miami, FL: MedMaster.
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